難治性の肝・胆道疾患に関する調査研究 厚生労働省難治性疾患政策研究事業

研究の成果

小児の門脈血行異常症

最終更新日:2022年6月2日
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  2. Nakajima Y, Yamazaki Y, Gao X, Hashimoto M, Nio M, Wada M, Fujishima F, Sasano H. Association between mitochondrial and nuclear DNA damages and cellular senescence in the patients with biliary atresia undergoing Kasai portoenterostomy and liver transplantation. Med Mol Morphol. 2022 Mar 3. doi: 10.1007/s00795-022-00314-z. Online ahead of print. https://pubmed.ncbi.nlm.nih.gov/35238992/
  3. Sakaguchi H, Konishi KI, Yasuda R, Sasaki H, Yoshimaru K, Tainaka T, Fukahori S, Sanada Y, Iwama I, Shoji H, Kinoshita M, Matsuura T, Fujishiro J, Uchida H, Nio M, Yamashita Y, Mizuochi T. Serum matrix metalloproteinase-7 in biliary atresia: A Japanese multicenter study. Hepatol Res. 2022 Feb 1. doi: 10.1111/hepr.13753. Online ahead of print. https://pubmed.ncbi.nlm.nih.gov/35106887/
  4. Sakamoto S, Hashizume N, Yagi M, Sasaki H, Nio M; Japanese Biliary Atresia Society. Postoperative pharmacotherapy for patients with biliary atresia in Japan. Pediatr Int. 2022 Jan;64(1):e14990. doi: 10.1111/ped.14990. https://pubmed.ncbi.nlm.nih.gov/34528345/
  5. Kawano T, Souzaki R, Sumida W, Shimojima N, Hishiki T, Kinoshita Y, Uchida H, Tajiri T, Yoneda A, Oue T, Kuroda T, Hirobe S, Koshinaga T, Hiyama E, Nio M, Inomata Y, Taguchi T, Ieiri S. Current thoracoscopic approach for mediastinal neuroblastoma in Japan-results from nationwide multicenter survey. Pediatr Surg Int. 2021 Dec;37(12):1651-1658. doi: 10.1007/s00383-021-04998-9. Epub 2021 Aug 27. https://pubmed.ncbi.nlm.nih.gov/34448929/
  6. Kudo H, Wada M, Sasaki H, Fukuzawa T, Ando R, Okubo R, Hashimoto M, Endo Y, Tada K, Nakajima Y, Nakamura M, Yamaki S, Nio M. Intestinal Transplantation at a Single Institution in Japan. Transplant Proc. 2021 Jul-Aug;53(6):2040-2045. doi: 10.1016/j.transproceed.2021.06.021. Epub 2021 Jul 12. https://pubmed.ncbi.nlm.nih.gov/34266655/
  7. Hashimoto M, Fujishima F, Lomphithak T, Jitkaew S, Nio M, Sasano H. Necroptosis in biliary atresia of the liver. Med Mol Morphol. 2021 Dec;54(4):305-315. doi: 10.1007/s00795-021-00289-3. Epub 2021 Jun 22. https://pubmed.ncbi.nlm.nih.gov/34159444/
  8. Kawano T, Souzaki R, Sumida W, Ishimaru T, Fujishiro J, Hishiki T, Kinoshita Y, Kawashima H, Uchida H, Tajiri T, Yoneda A, Oue T, Kuroda T, Koshinaga T, Hiyama E, Nio M, Inomata Y, Taguchi T, Ieiri S. Laparoscopic approach for abdominal neuroblastoma in Japan: results from nationwide multicenter survey. Surg Endosc. 2021 Jun 18. doi: 10.1007/s00464-021-08599-4. Online ahead of print. https://pubmed.ncbi.nlm.nih.gov/34143289/
  9. Sasaki H, Nio M, Ando H, Kitagawa H, Kubota M, Suzuki T, Taguchi T, Hashimoto T; Japanese Biliary Atresia Society. Anatomical patterns of biliary atresia including hepatic radicles at the porta hepatis influence short- and long-term prognoses. J Hepatobiliary Pancreat Sci. 2021 Nov;28(11):931-941. doi: 10.1002/jhbp.989. Epub 2021 Jul 1. https://pubmed.ncbi.nlm.nih.gov/34110698/
  10. Konishi KI, Mizuochi T, Takei H, Yasuda R, Sakaguchi H, Ishihara J, Takaki Y, Kinoshita M, Hashizume N, Fukahori S, Shoji H, Miyano G, Yoshimaru K, Matsuura T, Sanada Y, Tainaka T, Uchida H, Kubo Y, Tanaka H, Sasaki H, Murai T, Fujishiro J, Yamashita Y, Nio M, Nittono H, Kimura A. A Japanese prospective multicenter study of urinary oxysterols in biliary atresia. Sci Rep. 2021 Mar 2;11(1):4986. doi: 10.1038/s41598-021-84445-w. https://pubmed.ncbi.nlm.nih.gov/33654186/
  11. Okubo R, Nio M, Sasaki H; Japanese Biliary Atresia Society. Impacts of Early Kasai Portoenterostomy on Short-Term and Long-Term Outcomes of Biliary Atresia. Hepatol Commun. 2020 Nov 8;5(2):234-243. doi: 10.1002/hep4.1615. eCollection 2021 Feb. https://pubmed.ncbi.nlm.nih.gov/33553971/
  12. Watanabe T, Asawa Y, Watanabe M, Okubo R, Nio M, Takato T, Hoshi K, Hikita A. The usefulness of the decellularized matrix from three-dimensional regenerative cartilage as a scaffold material. Regen Ther. 2020 Dec 10;15:312-322. doi: 10.1016/j.reth.2020.11.005. eCollection 2020 Dec. https://pubmed.ncbi.nlm.nih.gov/33426234/
  13. Sakurai T, Okuyama Y, Kobayashi S, Phung HT, Asao A, Kawabe T, Ndhlovu LC, Riccardi C, Kudo H, Wada M, Nio M, So T, Ishii N. GITR controls intestinal inflammation by suppressing IL-15-dependent NK cell activity. FASEB J. 2020 Nov;34(11):14820-14831. doi: 10.1096/fj.202001675R. Epub 2020 Sep 10. https://pubmed.ncbi.nlm.nih.gov/32910505/
  14. Ando H, Inomata Y, Iwanaka T, Kuroda T, Nio M, Matsui A, Yoshida M; Japanese Biliary Atresia Society. Clinical practice guidelines for biliary atresia in Japan: A secondary publication of the abbreviated version translated into English. J Hepatobiliary Pancreat Sci, 2021 Jan;28(1):55-61. doi: 10.1002/jhbp.816. Epub 2020 Oct 4. https://pubmed.ncbi.nlm.nih.gov/32780928/
  15. Uchida H, Sakamoto S, Kasahara M, Kudo H, Okajima H, Nio M, Umeshita K, Ohdan H, Egawa H, Uemoto S; Japanese Liver Transplantation Society. Longterm Outcome of Liver Transplantation for Congenital Extrahepatic Portosystemic Shunt. Liver Transpl, 2021 Feb;27(2):236-247. doi: 10.1002/lt.25805. Epub 2020 Aug 6. https://pubmed.ncbi.nlm.nih.gov/32463947/
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